Basicmedical Key

Juxtaarticular Myxoma Khin Thway, BSc, MBBS, FRCPath Key Facts Terminology Benign lesion occurring in region of large joints, with histologic features of myxoma Etiology/Pathogenesis Some associated with trauma or occur…

Intramuscular Myxoma Khin Thway, BSc, MBBS, FRCPath Key Facts Terminology Benign soft tissue tumor composed of bland spindle to stellate fibroblasts within abundant extracellular myxoid matrix Clinical Issues Middle-aged adults…

Angiosarcoma of Soft Tissue Thomas Mentzel, MD Key Facts Terminology Malignant mesenchymal neoplasm of cells recapitulating variably morphologic and functional features composed of endothelial cells Clinical Issues Deep soft tissues…

Cutaneous Angiosarcoma Thomas Mentzel, MD Key Facts Terminology Malignant mesenchymal neoplasm of cells variably recapitulating morphologic and functional features composed of endothelial cells Etiology/Pathogenesis Idiopathic (actinic) angiosarcoma Predominantly in actinically…

Kaposi Sarcoma Thomas Mentzel, MD Key Facts Terminology Locally aggressive endothelial neoplasm associated with human herpes virus 8 Clinical Issues Most typical site of involvement is skin Mucosal membranes, lymph…

Epithelioid Hemangioendothelioma Thomas Mentzel, MD Key Facts Terminology Vascular neoplasm with metastatic potential composed of epithelioid endothelial cells Clinical Issues Rare vascular tumor Superficial or deep soft tissue Rare in…

Epithelioid Sarcoma-Like Hemangioendothelioma Steven D. Billings, MD Key Facts Terminology Vascular tumor of apparent intermediate malignancy that histologically closely resembles epithelioid sarcoma Clinical Issues Presents most commonly in young adults…

Papillary Intralymphatic Angioendothelioma (Dabska) David S. Cassarino, MD, PhD Julie C. Fanburg-Smith, MD Key Facts Terminology Dabska tumor Endovascular papillary angioendothelioma Clinical Issues Typically occur in children (minority in adults)…

Atypical Vascular Proliferation Thomas Mentzel, MD Key Facts Terminology Vascular proliferation after radiotherapy excluding obvious post-irradiation angiosarcoma, arising predominantly in breast Clinical Issues Exact incidence is difficult to establish Occurs…

Kaposiform Hemangioendothelioma Steven D. Billings, MD Key Facts Clinical Issues Presents in infants and young children Associated with Kasabach-Merritt syndrome (especially retroperitoneal tumors) Consumptive coagulopathy Thrombocytopenia Rare regional lymph node…