Retiform Hemangioendothelioma
More common in children
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Composite hemangioendothelioma (HE)
Composed of at least 2 distinct HE types
TERMINOLOGY
Abbreviations
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Retiform hemangioendothelioma (RHE)
Synonyms
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Hobnail hemangioendothelioma (HE)
Definitions
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Low-grade malignant vascular tumor composed of elongated vessels resembling rete testis
ETIOLOGY/PATHOGENESIS
Unknown
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Rare cases associated with lymphedema or preceding radiation
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1 case reported to be positive for HHV8
CLINICAL ISSUES
Epidemiology
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Incidence
Rare vascular tumor
•
Age
Typically middle-aged adults but may occur in children
•
Sex
More common in females
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