Infantile Fibrosarcoma
Infantile Fibrosarcoma Thomas Mentzel, MD Key Facts Terminology Occurs in infants and young children; represents low-grade fibrosarcoma that carries favorable prognosis Clinical Issues Congenital or arises in 1st two years…
Solitary Fibrous Tumor
Solitary Fibrous Tumor Khin Thway, BSc, MBBS, FRCPath Key Facts Terminology Fibroblastic mesenchymal tumor with prominent hemangiopericytic branching vascular pattern Initially described in pleura Occur in any location Closely related…
Fibromatosis
Fibromatosis Elizabeth A. Montgomery, MD Key Facts Terminology Palmar fibromatosis: Dupuytren contracture, Dupuytren disease Plantar fibromatosis: Ledderhose disease Penile fibromatosis: Peyronie disease Deep fibromatosis: Aggressive fibromatosis, desmoid tumor Myofibroblastic proliferations…
Lipofibromatosis
Lipofibromatosis Elizabeth A. Montgomery, MD Key Facts Clinical Issues Painless mass Hands and feet of children Median age: 1 year Male predominance (M:F = 2:1) Local recurrences common No metastases…
Nasopharyngeal Angiofibroma
Nasopharyngeal Angiofibroma Lester Thompson, MD Cyril Fisher, MD, DSc, FRCPath Key Facts Terminology Benign, highly cellular, and richly vascularized mesenchymal neoplasm arising in nasopharynx in males Clinical Issues Recurrent, spontaneous…
Giant Cell Angiofibroma
Giant Cell Angiofibroma Amitabh Srivastava, MD Key Facts Terminology Benign fibroblastic tumor with multinucleated tumor giant cells and angiectoid spaces May be related to solitary fibrous tumor/hemangiopericytoma group Clinical Issues…
Dermatomyofibroma
Dermatomyofibroma David S. Cassarino, MD, PhD Key Facts Terminology Myofibroblastic tumor with features overlapping with dermatofibroma Clinical Issues Slow-growing plaque or nodule Microscopic Pathology Dermal-based spindle cell proliferation Tumor is…
Fibrous Hamartoma of Infancy
Fibrous Hamartoma of Infancy Khin Thway, BSc, MBBS, FRCPath Key Facts Terminology Benign superficial fibrous lesion occurring during 1st 2 years of life Clinical Issues Congenital in up to 25%…
Ischemic Fasciitis
Ischemic Fasciitis Elizabeth A. Montgomery, MD Key Facts Terminology Pseudosarcomatous proliferation Clinical Issues Mean age: 8th decade Most cases do not recur following excision Microscopic Pathology Most involve deep subcutis…
Nodular Fasciitis
Nodular Fasciitis Elizabeth A. Montgomery, MD Key Facts Clinical Issues Age: 3rd-4th decades Gender: M = F Most lesions are benign and do not recur, even if incompletely excised Simple…
