Epithelioid Hemangioendothelioma Key Facts Terminology Epithelioid hemangioendothelioma (EH) Synonym: Intravascular bronchioloalveolar tumor (IVBT) Clinical Issues Incidence Unusual tumor in lung Appears to be more common in young adults; age range:…
Acinic Cell Carcinoma Key Facts Terminology Fechner tumor Epithelial neoplasm similar to that in salivary glands Clinical Issues Cough Chest Pain Asymptomatic Macroscopic Features Necrosis and hemorrhage are not common…
Kaposi Sarcoma Key Facts Etiology/Pathogenesis Commonly associated with HIV infection in patients with AIDS Associated with human herpes virus 8 (HHV-8) infection Clinical Issues High incidence in homosexual men and…
Leiomyosarcoma Key Facts Clinical Issues Incidence Represents < 1% of all malignant neoplasms of lung Described in any age group from newborns to adults Symptoms Cough Hemoptysis Chest pain Dyspnea…
Adenoid Cystic Carcinoma Key Facts Terminology Epithelial neoplasm similar to that occurring in salivary glands Clinical Issues Presentation Cough, hemoptysis, dyspnea, chest pain Treatment Lobectomy or pneumonectomy Pathogenesis May follow…
Intrapulmonary Synovial Sarcoma Key Facts Clinical Issues Chest pain Shortness of breath Cough Aggressive behavior with frequent recurrences and metastases Macroscopic Features Well-circumscribed, unencapsulated, solitary mass within lung parenchyma Tan-white…
Neurogenic Sarcoma (Malignant Peripheral Nerve Sheath Tumor) Key Facts Clinical Issues Extremely rare tumor Often associated with neurofibromatosis Tumors may be central or peripheral Tumors may arise in endobronchial location…
Carcinosarcoma Key Facts Terminology Malignant biphasic neoplasm composed of malignant epithelial and malignant mesenchymal components Etiology/Pathogenesis Carcinosarcomas have been linked to tobacco use Clinical Issues More common in men than…
Pulmonary Blastoma Key Facts Terminology Synonyms: Well-differentiated fetal adenocarcinoma, pulmonary embryoma PB monophasic type (well-differentiated fetal adenocarcinoma): Glandular component recapitulates embryonic development of lung PB biphasic type: Composed of epithelial…
Large Cell (Anaplastic) Carcinoma Key Facts Clinical Issues Cough Chest pain Dyspnea Generally poor prognosis with short survival Most commonly seen in smokers Image Findings Periphery of lungs Generally large…
