Juvenile Hyaline Fibromatosis



Juvenile Hyaline Fibromatosis


Elizabeth A. Montgomery, MD

Cyril Fisher, MD, DSc, FRCPath









Hematoxylin & eosin shows juvenile hyaline fibromatosis of face in subepithelial tissue image. There is a tumor-free (Grenz) zone image between the epidermis and the lesional tissue.






Hematoxylin & eosin shows scattered lesional cells in homogeneous eosinophilic stroma. The cells are small and uniform, arranged in short curved cords image. Some nuclei appear in spaces image.


TERMINOLOGY


Abbreviations



  • Juvenile hyaline fibromatosis (JHF)


Synonyms



  • Related disorder: Infantile systemic hyalinosis (ISH)



    • Suggested synonym: Hyaline fibromatosis syndrome


Definitions



  • Rare autosomal recessive disorder (often found in consanguineous populations) characterized by multiple skin papules and early onset

Jul 9, 2016 | Posted by in PATHOLOGY & LABORATORY MEDICINE | Comments Off on Juvenile Hyaline Fibromatosis
Premium Wordpress Themes by UFO Themes
%d bloggers like this: