Diseases of the Circulatory System
(ICD-10-CM Chapter 9, Codes I00-I99)
Learning Objectives
2. Identify pertinent anatomy and physiology of the circulatory system
3. Identify diseases of the circulatory system
4. Assign the correct Z codes and procedure codes related to the circulatory system
5. Identify common treatments, medications, laboratory values, and diagnostic tests
6. Explain the importance of documentation in relation to MS-DRGs for reimbursement
Abbreviations/Acronyms
AICD automatic implantable cardioverter-defibrillator
AIDS acquired immunodeficiency syndrome
AMI acute myocardial infarction
AVM arteriovenous malformation
CABG coronary artery bypass graft
CAT computerized axial tomography
COPD chronic obstructive pulmonary disease
CPK-MB creatine phosphokinase, isoenzyme MB
CRT cardiac resynchronization therapy
CRT-D cardiac resynchronization treatment defibrillator
CRT-P cardiac resynchronization treatment pacemaker
CXR chest x-ray
EKG/ECG electrocardiogram
HCVD hypertensive cardiovascular disease
HTN hypertension
ICD internal cardiac defibrillator
ICD-9-CM International Classification of Diseases, 9th Revision, Clinical Modification
ICD-10-CM International Classification of Diseases, 10th Revision, Clinical Modification
ICD-10-PCS International Classification of Diseases, 10th Revision, Procedure Coding System
IV intravenous
MRI magnetic resonance imaging
MS-DRG Medicare Severity diagnosis-related group
MUGA multiple-gated acquisition
NQMI non–Q wave myocardial infarction
NSTEMI non–ST elevation myocardial infarction
PCI percutaneous coronary intervention
PDA posterior descending artery
PICC peripherally inserted central catheter
PPH primary pulmonary hypertension
PTCA percutaneous transluminal coronary angioplasty
RA right atrium
RBBB right bundle branch block
STEMI ST elevation myocardial infarction
SVT supraventricular tachycardia
TPA tissue plasminogen activator
TPN total parenteral nutrition
USA unstable angina
ICD-10-CM Official Guidelines for Coding and Reporting
Please refer to the companion Evolve website for the most current guidelines.
9. Chapter 9: Diseases of Circulatory System (I00-I99)
a. Hypertension
1) Hypertension with Heart Disease
Heart conditions classified to I50.- or I51.4-I51.9, are assigned to, a code from category I11, Hypertensive heart disease, when a causal relationship is stated (due to hypertension) or implied (hypertensive). Use an additional code from category I50, Heart failure, to identify the type of heart failure in those patients with heart failure.
The same heart conditions (I50.-, I51.4-I51.9) with hypertension, but without a stated causal relationship, are coded separately. Sequence according to the circumstances of the admission/encounter.
2) Hypertensive Chronic Kidney Disease
Assign codes from category I12, Hypertensive chronic kidney disease, when both hypertension and a condition classifiable to category N18, Chronic kidney disease (CKD), are present. Unlike hypertension with heart disease, ICD-10-CM presumes a cause-and-effect relationship and classifies chronic kidney disease with hypertension as hypertensive chronic kidney disease.
The appropriate code from category N18 should be used as a secondary code with a code from category I12 to identify the stage of chronic kidney disease.
See Section I.C.14. Chronic kidney disease.
If a patient has hypertensive chronic kidney disease and acute renal failure, an additional code for the acute renal failure is required.
3) Hypertensive Heart and Chronic Kidney Disease
Assign codes from combination category I13, Hypertensive heart and chronic kidney disease, when both hypertensive kidney disease and hypertensive heart disease are stated in the diagnosis. Assume a relationship between the hypertension and the chronic kidney disease, whether or not the condition is so designated. If heart failure is present, assign an additional code from category I50 to identify the type of heart failure.
The appropriate code from category N18, Chronic kidney disease, should be used as a secondary code with a code from category I13 to identify the stage of chronic kidney disease.
See Section I.C.14. Chronic kidney disease.
The codes in category I13, Hypertensive heart and chronic kidney disease, are combination codes that include hypertension, heart disease and chronic kidney disease. The Includes note at I13 specifies that the conditions included at I11 and I12 are included together in I13. If a patient has hypertension, heart disease and chronic kidney disease then a code from I13 should be used, not individual codes for hypertension, heart disease and chronic kidney disease, or codes from I11 or I12.
For patients with both acute renal failure and chronic kidney disease an additional code for acute renal failure is required.
4) Hypertensive Cerebrovascular Disease
For hypertensive cerebrovascular disease, first assign the appropriate code from categories I60-I69, followed by the appropriate hypertension code.
5) Hypertensive Retinopathy
Subcategory H35.0, Background retinopathy and retinal vascular changes, should be used with a code from category I10 – I15, Hypertensive disease to include the systemic hypertension. The sequencing is based on the reason for the encounter.
6) Hypertension, Secondary
Secondary hypertension is due to an underlying condition. Two codes are required: one to identify the underlying etiology and one from category I15 to identify the hypertension. Sequencing of codes is determined by the reason for admission/encounter.
7) Hypertension, Transient
Assign code R03.0, Elevated blood pressure reading without diagnosis of hypertension, unless patient has an established diagnosis of hypertension. Assign code O13.-, Gestational [pregnancy-induced] hypertension without significant proteinuria, or O14.-, Pre-eclampsia, for transient hypertension of pregnancy.
8) Hypertension, Controlled
This diagnostic statement usually refers to an existing state of hypertension under control by therapy. Assign the appropriate code from categories I10-I15, Hypertensive diseases.
9) Hypertension, Uncontrolled
Uncontrolled hypertension may refer to untreated hypertension or hypertension not responding to current therapeutic regimen. In either case, assign the appropriate code from categories I10-I15, Hypertensive diseases.
b. Atherosclerotic Coronary Artery Disease and Angina
ICD-10-CM has combination codes for atherosclerotic heart disease with angina pectoris. The subcategories for these codes are I25.11, Atherosclerotic heart disease of native coronary artery with angina pectoris and I25.7, Atherosclerosis of coronary artery bypass graft(s) and coronary artery of transplanted heart with angina pectoris.
When using one of these combination codes it is not necessary to use an additional code for angina pectoris. A causal relationship can be assumed in a patient with both atherosclerosis and angina pectoris, unless the documentation indicates the angina is due to something other than the atherosclerosis.
If a patient with coronary artery disease is admitted due to an acute myocardial infarction (AMI), the AMI should be sequenced before the coronary artery disease.
See Section I.C.9. Acute myocardial infarction (AMI)
c. Intraoperative and Postprocedural Cerebrovascular Accident
Medical record documentation should clearly specify the cause- and-effect relationship between the medical intervention and the cerebrovascular accident in order to assign a code for intraoperative or postprocedural cerebrovascular accident.
Proper code assignment depends on whether it was an infarction or hemorrhage and whether it occurred intraoperatively or postoperatively. If it was a cerebral hemorrhage, code assignment depends on the type of procedure performed.
d. Sequelae of Cerebrovascular Disease
1) Category I69, Sequelae of Cerebrovascular disease
Category I69 is used to indicate conditions classifiable to categories I60-I67 as the causes of sequela (neurologic deficits), themselves classified elsewhere. These “late effects” include neurologic deficits that persist after initial onset of conditions classifiable to categories I60-I67. The neurologic deficits caused by cerebrovascular disease may be present from the onset or may arise at any time after the onset of the condition classifiable to categories I60-I67.
Codes from category I69, Sequelae of cerebrovascular disease, that specify hemiplegia, hemiparesi, and monoplegia identify whether the dominant or nondominant side is affected. Should the affected side be documented but not specified as dominant or nondominant, and the classification system does not indicate a default, code selection is as follows:
• For ambidextrous patients, the default should be dominant.
• If the left side is affected, the default is non-dominant.
• If the right side is affected, the default is dominant.
2) Codes from category I69 with codes from I60-I67
Codes from category I69 may be assigned on a health care record with codes from I60-I67, if the patient has a current cerebrovascular disease and deficits from an old cerebrovascular disease.
3) Codes from category I69 and Personal history of transient ischemic attack (TIA) and cerebral infarction (Z86.73)
Codes from category I69 should not be assigned if the patient does not have neurologic deficits.
See Section I.C.21. 4. History (of) for use of personal history codes
e. Acute myocardial infarction (AMI)
1) ST elevation myocardial infarction (STEMI) and non ST elevation myocardial infarction (NSTEMI)
The ICD-10-CM codes for acute myocardial infarction (AMI) identify the site, such as anterolateral wall or true posterior wall. Subcategories I21.0-I21.2 and code I21.4 are used for ST elevation myocardial infarction (STEMI). Code I21.4, Non-ST elevation (NSTEMI) myocardial infarction, is used for non ST elevation myocardial infarction (NSTEMI) and nontransmural MIs.
If NSTEMI evolves to STEMI, assign the STEMI code. If STEMI converts to NSTEMI due to thrombolytic therapy, it is still coded as STEMI.
For encounters occurring while the myocardial infarction is equal to, or less than, four weeks old, including transfers to another acute setting or a postacute setting, and the patient requires continued care for the myocardial infarction, codes from category I21 may continue to be reported. For encounters after the 4 week time frame and the patient is still receiving care related to the myocardial infarction, the appropriate aftercare code should be assigned, rather than a code from category I21. For old or healed myocardial infarctions not requiring further care, code I25.2, Old myocardial infarction, may be assigned.
2) Acute myocardial infarction, unspecified
Code I21.3, ST elevation (STEMI) myocardial infarction of unspecified site, is the default for the unspecified term acute myocardial infarction. If only STEMI or transmural MI without the site is documented, query the provider as to the site, or assign code I21.3.
3) AMI documented as nontransmural or subendocardial but site provided
If an AMI is documented as nontransmural or subendocardial, but the site is provided, it is still coded as a subendocardial AMI. If NSTEMI evolves to STEMI, assign the STEMI code. If STEMI converts to NSTEMI due to thrombolytic therapy, it is still coded as STEMI.
See Section I.C.21.3 for information on coding status post administration of tPA in a different facility within the last 24 hours.
4) Subsequent acute myocardial infarction
A code from category I22, Subsequent ST elevation (STEMI) and non ST elevation (NSTEMI) myocardial infarction, is to be used when a patient who has suffered an AMI has a new AMI within the 4 week time frame of the initial AMI. A code from category I22 must be used in conjunction with a code from category I21. The sequencing of the I22 and I21 codes depends on the circumstances of the encounter.
Apply the General Coding Guidelines as found in Chapter 5 and the Procedural Coding Guidelines as found in Chapters 6 and 7.
Anatomy and Physiology
The circulatory system is composed of the heart and blood vessels (Figure 15-1). Its function is to supply tissue in the body with oxygen and nutrients. This function is accomplished when the arteries carry blood (oxygen) to the cells. The largest artery, the aorta, branches off the heart and divides into many smaller arteries. The veins carry deoxygenated blood to the lungs to acquire oxygen and then to the heart, which pumps oxygenated blood back to the arteries.
The Heart
The function of the heart is to pump oxygen-rich blood to the cells of the body. The heart itself receives oxygenated blood from the coronary arteries; the two major coronary arteries branch off the aorta.
The heart is enclosed laterally by the lungs, posteriorly by the backbone, and anteriorly by the sternum. The wall of the heart is composed of three layers: epicardium, myocardium, and endocardium (Figure 15-2). The epicardium is the outer protective layer, the myocardium is the middle layer and is composed of cardiac muscle, and the endocardium is the inner layer that lines all the heart chambers and covers the heart valves.
The heart consists of four chambers: right atrium, left atrium, right ventricle, and left ventricle. The atrium and the ventricle on the right side are separated from the left by a septum. The top two chambers, the atria, receive blood via the veins from the body or the lungs. The right ventricle pumps blood to the lungs to pick up oxygen, and the left ventricle pumps blood to the rest of the body. Within the heart are four valves (Figure 15-3), and their job is to direct blood flow. The tricuspid valve is located between the right atrium and the right ventricle. The valve between the left atrium and the left ventricle is the mitral or bicuspid valve. The aortic valve is located in the aorta at the point at which the left ventricle empties into the aorta. The pulmonary valve is located in the pulmonary artery at the point of exit from the right ventricle.
Blood Vessels
Blood vessels are the tubes that transport blood from the heart to the cells and back to the heart. Most arteries (Figure 15-4) carry oxygenated blood away from the heart. They continue to get smaller the farther away they are from the heart (arterioles). At this point, arterioles lead to capillaries, and exchange is made between blood and body cells; venules and veins (Figure 15-5) return blood back to the heart. The circulation of blood that moves throughout the body is referred to as systemic circulation. Blood pressure measured at the arm indicates systemic pressures.
Lymphatic System
The lymphatic system is closely related to the circulatory system. The lymphatic drainage system returns back to the bloodstream products that have leaked out from the capillaries. The lymph system is made up of lymph nodes, as well as spleen, thymus, tonsils, and adenoids. The lymph system fights infection by filtering out viruses and bacteria by attacking them with lymphocytes.
Disease Conditions
Diseases of the Circulatory System (I00-I99), Chapter 9 in the ICD-10-CM code book, is divided into the following categories:
CATEGORY | SECTION TITLES |
I00-I02 | Acute rheumatic fever |
I05-I09 | Chronic rheumatic heart disease |
I10-I15 | Hypertensive diseases |
I20-I25 | Ischemic heart diseases |
I26-I28 | Pulmonary heart disease and diseases of pulmonary circulation |
I30-I52 | Other forms of heart disease |
I60-I69 | Cerebrovascular diseases |
I70-I79 | Diseases of arteries, arterioles, and capillaries |
I80-I89 | Diseases of veins, lymphatic vessels, and lymph nodes, not elsewhere classified |
I95-I99 | Other and unspecified disorders of the circulatory system |
Acute Rheumatic Fever (I00-I02) and Chronic Rheumatic Heart Disease (I05-I09)
Acute rheumatic fever is an inflammatory disease usually found in children that may affect the heart, joints, skin, or brain following an infection with streptococcal bacteria such as strep throat or scarlet fever.
Chronic rheumatic heart disease is a chronic condition that is usually a late effect of attacks of acute rheumatic fever and most often involves the heart valves. When mitral and aortic valves are involved, ICD-10-CM assumes a causal relationship to rheumatic heart disease unless specified as nonrheumatic. ICD-10-CM also presumes a causal relationship for certain mitral valve disorders of unspecified etiology. Tricuspid valve disorders are assumed rheumatic unless specified as nonrheumatic in origin (Figure 15-6).
Hypertensive Diseases (I10-I15)
Hypertension is classified as primary (essential) or secondary. Primary hypertension, or high blood pressure (BP), is a condition that is defined as abnormally high blood pressure in the arterial system. The American Heart Association defines hypertension as pressures exceeding 140/90. A diagnosis of hypertension can be made only by a physician and should not be assigned on the basis of BP readings alone. Essential hypertension has no known origin, and its symptoms are insidious.
Secondary hypertension is a consequence of other diseases such as kidney diseases, brain tumor, or polycythemia. When secondary hypertension is documented, two codes are required. The additional code required for secondary hypertension is the underlying condition code. The sequencing of these two codes depends on the circumstances of the admission.
Medications often used for treating hypertension include Accupril, Aldomet, captopril, Cardizem, diltiazem, Cozaar, losartan, Coreg, dyazide, Hytrin, Inderal, Lopressor, Norvasc, Procardia, Tenormin, atenolol, Vasotec, Toprol, Calan, verapamil, Zestril, and lisinopril.
For a variety of reasons, patients may have elevated blood pressure readings. Unless a patient has an established diagnosis of hypertension, the code R03.0 elevated blood pressure, should be assigned.
Hypertensive Heart, Renal, and Heart and Renal Disease
ICD-10-CM assumes a cause-and-effect relationship and classifies chronic kidney disease with hypertension as hypertensive renal disease. This indicates to the coder that any time hypertension and chronic kidney disease (codes from category N18) occur in a patient, category (I12) should be assigned. The only time the (I12) category code would not be selected is when the physician documents CKD not due to hypertension. On occasion, a patient will have CKD due to diabetes and also have hypertension; diabetic kidney disease and hypertensive kidney disease would both be assigned in these cases.
Hypertensive heart disease, in contrast to hypertensive renal disease, does not assume a cause-and-effect relationship. A causal relationship must be stated by the physician. For a code from this category to be assigned, the physician must document hypertensive heart disease or must say that heart disease is due to hypertension. It is important to note that if a patient has hypertensive congestive heart failure, at least two codes—I11.0 and I50.- —are required; if known, the codes for systolic (I50.2-), diastolic (I50.3-), or a combination systolic and diastolic (I50.4-) should also be assigned.
Hypertensive heart and renal disease requires that the condition be classified to I13.–. It is important to become familiar with the Includes as well as Excludes notes in all of the above categories. It is also important to note that if a patient also has acute renal failure with any of the above conditions, an additional code for the acute renal failure is also assigned.
Exercise 15-1
Assign codes to the following conditions.
1. Patient is admitted with a diagnosis of hypertensive urgency | _______________ |
2. Aortic stenosis with mitral insufficiency | _______________ |
3. Malignant hypertension | _______________ |
4. Labile hypertension | _______________ |
5. Portal hypertension | _______________ |
6. Congestive heart failure due to hypertensive heart disease | _______________ |
7. Cardiomegaly with hypertension | _______________ |
8. Hypertension secondary to coarctation of aorta | _______________ |
9. Ocular hypertension, right eye | _______________ |
10. Essential hypertension | _______________ |
11. HCVD (hypertensive cardiovascular disease) with chronic renal failure | _______________ |
12. High blood pressure reading | _______________ |
Ischemic Heart Disease (I20-I25)
Acute Myocardial Infarction
Acute myocardial infarction (AMI, or MI) in layman’s terms is known as a heart attack. An MI occurs when complete blockage of blood flow occurs in a coronary artery. When this occurs, blood is prevented from reaching the heart muscle (Figure 15-7). Blockage may be caused by fatty deposits (also known as plaque or atherosclerosis) or blood clots. When the blood cannot reach the heart, the heart muscle may become damaged. Signs of a heart attack include chest pain, shortness of breath, nausea, and pain in the arms and chest.
To determine whether a patient is having a heart attack, several tests, including various types of blood tests, may be performed. One of these tests is called CPK (creatine phosphokinase, or creatine kinase). CPK is an isoenzyme that occurs in high concentration in the heart and skeletal muscle. The level of CPK-MB (creatine phosphokinase, MB isoenzyme) in the blood rises 3 to 6 hours after an MI and returns to normal 12 to 48 hours after the infarct. Usually, CPK is measured every 8 to 12 hours, and patterns are determined. The normal value for males is 25 to 90; for females, it is 10 to 70. Another type of blood test that is often performed is the measurement of cardiac muscle proteins called troponins. Testing for troponin levels and CPK levels is performed serially. Troponin levels are usually very low, and elevated levels can indicate damage to the heart. Healthcare providers also perform electrocardiograms (EKGs) to determine whether an MI has occurred.
Types of MI may be classified as to the area of heart that suffers damage or the extent of damage, as evidenced by an EKG (Figure 15-8). The most common areas are the following:
STEMI (ST elevation MI) occurs when complete obstruction of the coronary artery causes damage involving the full thickness of the heart muscle. This type of MI is also known as an ST elevation MI or a Q wave MI. NSTEMI (non–ST elevation) occurs when a coronary artery is partially obstructed and damage does not involve the full thickness of the heart muscle. This type of MI is often referred to as non–Q wave MI. Old terminology for transmural or nontransmural MI has been replaced by Q or non–Q MI.
Patients suspected of having an MI are usually treated with a combination of medications and/or procedures. Procedures performed to treat the causes of MI include coronary angioplasty (percutaneous transluminal coronary angioplasty [PTCA]), stenting (percutaneous coronary intervention [PCI]), and possibly coronary artery bypass surgery (CABG or CAB). Often, upon presentation of the patient to the Emergency Room (ER), thrombolytic therapy is initiated. Thrombolytics (tissue plasminogen activator [TPA], streptokinase) are used to dissolve blood clots that may be blocking a coronary artery. Thrombolytics must be administered within 6 hours of the onset of chest pain to avoid heart damage. A potential adverse effect of the use of these drugs is severe bleeding; for this reason, they are contraindicated in many patients. All of these procedures are discussed in greater detail in the procedure section of this chapter.
When assigning a code for an acute MI in ICD-10-CM, it is important to find documentation of the site of the MI for a STEMI. It is also important to note that a code from I21 is assigned for an MI that has occurred within 28 days of the current admission. If the MI is older than 28 days, then code I25.2 is assigned.